PENATALAKSANAAN SINDROMA MAYER ROKITANSKY KUSTER HAUSER (SINDROMA MRKH) DENGAN SINDROMA KLIPPEL FEIL
نویسندگان
چکیده
منابع مشابه
Mayer-Rokitansky-Kuster-Hauser Syndrome.
Mayer-Rokitansky-Küster-Hauser Syndrome is a congenital malformation in which there is failure of the Müllerian ducts to develop resulting in absent uterus and fallopian tubes and variable malformations of the vagina. Ultrasonography reveals absence of uterus with normally visualised ovaries.
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The congenital aplasia or severe hypoplasia of mullerian structures is infrequent. However, the features of normal female endocrine function paired with the absence of a functional uterus and vagina makes it a fascinating entity. The diagnosis and work-up in these patients has become very efficient, thanks to the use of imaging, and there are multiple successful procedures for the creation of a...
متن کاملMayer-Rokitansky-Küster-Hauser (MRKH) syndrome
The Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by congenital aplasia of the uterus and the upper part (2/3) of the vagina in women showing normal development of secondary sexual characteristics and a normal 46, XX karyotype. It affects at least 1 out of 4500 women. MRKH may be isolated (type I) but it is more frequently associated with renal, vertebral, and, to a lesser ext...
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MayerRokitanskyKusterHauser (MRKH) syndrome is a rare entity characterized by congenital aplasia of the uterus and the upper part of 2/3rd of vagina in normal karyotype females with normal development of secondary sexual characteristics. The incidence rate is about 1 in every 4500 females. We report a case series of three different patients who presented with different clinical picture to vario...
متن کاملMayer-Rokitansky-Kuster-Hauser (MRKH) syndrome: it's more than the anatomy.
2009 North Ame Published by Elsev How do you counsel a patient with vaginal agenesis? The scenario is something like this. You complete your evaluation and the concerned parent says, ‘‘Does that mean my daughter will never have children?’’ Well, then we move to ‘‘she can have her own genetic child’’ through assisted reproduction-in vitro fertilization with a surrogate carrier. So what are the o...
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ژورنال
عنوان ژورنال: Jurnal Kedokteran Brawijaya
سال: 2004
ISSN: 2338-0772
DOI: 10.21776/ub.jkb.2004.020.02.7